Característica clínica del Niño con Síndrome de West atendido en el Hospital "Dr. Roberto Gilbert Elizalde"

Abstract

Background: West síndrome (SW) is characterized by the presence of spasms in salvos, EEG tracing hypsarrhythmic , and detection or regression in the psychomotor development. Entity is a devastating epileptic infant whose prognosis has been linked to the etiology and treatment precocity. Objectives: To determine the clinical characteristics of children with West syndrome treated at the Hospital Roberto Gilbert Elizalde. Method: Retrospective study of 46 children diagnosed from 2000 to 2010 SW. Analysis: To describe the results of the study used simple frequencies, percentages and averages, for these values given a measure of dispersion of the mean 1 SD. Results: Female/male ratio: 1.19.1. Average age at the start of the spasm was 6.6 months (range 2 to 14 months9. Diganostico-therapeutic delay of less than 1 month 86.9%. Spasms in flexion predominated (61%). Debut 8 children (17.39%) with psychomotor retardation n prior to the crisis of spasm. Has a history of prenatal pathology 39% . Perinatal asphyxia was the most frequent diagnosis. The response to treatment in 525 of patients decreased the number of attacks of spasm, 31% no answer and 17% stopped the spasms. Evolved syndrome Lennox- Gastaut´s at 13.0%. Conclusion: The age of onset, gender, crisis and the prognosis in this patient group are similar to those presented in the literature. There remains a significant delay in diagnosis by the confusion of the “spasms” with other non-epileptic paroxysmal episodes. The evolution of these patients is strongly influenced by pre-existing injury, which influences the prognosis of children with West syndrome, in addition to the possible launch delayed clouding the future treatment and enhances neurological squealed associated with it.